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Early Fracture Healing is Delayed in the Col1a2 +/G610C Osteogenesis Imperfecta Murine Model 1-gen-2018 Besio, R; Maruelli, S; Battaglia, S; Leoni, L; Villani, S; Layrolle, P; Rossi, A; Trichet, V; Forlino, A
4-PBA ameliorates cellular homeostasis in fibroblasts from osteogenesis imperfecta patients by enhancing autophagy and stimulating protein secretion 1-gen-2018 Besio, R; Iula, G; Garibaldi, N; Cipolla, L; Sabbioneda, S; Biggiogera, M; Marini, Jc.; Rossi, A; Forlino, A
Bone biology: insights from osteogenesis imperfecta and related rare fragility syndromes 1-gen-2019 Besio, Roberta; Chow, Chi-Wing; Tonelli, Francesca; Marini, Joan C; Forlino, Antonella
Steady-state and pulse-chase analyses of fibrillar collagen 1-gen-2019 Forlino, A.; Tonelli, F.; Besio, R.
Absence of Dipeptidyl Peptidase 3 increases oxidative stress and causes bone loss 1-gen-2019 Menale, Ciro; Robinson, Lisa J; Palagano, Eleonora; Rigoni, Rosita; Erreni, Marco; Almarza, Alejandro J; Strina, Dario; Mantero, Stefano; Lizier, Michela; Forlino, Antonella; Besio, Roberta; Monari, Marta; Vezzoni, Paolo; Cassani, Barbara; Blair, Harry C; Villa, Anna; Sobacchi, Cristina
First person - Roberta Besio 1-gen-2019 Besio, R.
Cellular stress due to impairment of collagen prolyl hydroxylation complex is rescued by the chaperone 4-phenylbutyrate 1-gen-2019 Besio, R.; Garibaldi, Nadia; Leoni, Laura; Cipolla, L.; Sabbioneda, S.; Biggiogera, M.; Mottes, Monica; Aglan, M.; Otaify, G. A.; Temtamy, S. A.; Rossi, A.; Forlino, A.
Calcium activated nucleotidase 1 (CANT1) is critical for glycosaminoglycan biosynthesis in cartilage and endochondral ossification 1-gen-2019 Paganini, Chiara; Monti, Luca; Costantini, Rossella; Besio, Roberta; Lecci, Silvia; Biggiogera, Marco; Tian, Kun; Schwartz, Jean-Marc; Huber, Céline; Cormier-Daire, Valérie; Gibson, Beth G.; Pirog, Katarzyna A.; Forlino, Antonella; Rossi, Antonio
Crtap and p3h1 knock out zebrafish support defective collagen chaperoning as the cause of their osteogenesis imperfecta phenotype 1-gen-2020 Tonelli, F.; Cotti, S.; Leoni, L.; Besio, R.; Gioia, R.; Marchese, L.; Giorgetti, S.; Villani, S.; Gistelinck, C.; Wagener, R.; Kobbe, B.; Fiedler, I. A. K.; Larionova, D.; Busse, B.; Eyre, D.; Rossi, A.; Witten, P. E.; Forlino, A.
Osteoblasts mineralization and collagen matrix are conserved upon specific Col1a2 silencing 1-gen-2020 Maruelli, S.; Besio, R.; Rousseau, J.; Garibaldi, N.; Amiaud, J.; Brulin, B.; Layrolle, P.; Escriou, V.; Rossi, A.; Trichet, V.; Forlino, A.
Zebrafish: A Resourceful Vertebrate Model to Investigate Skeletal Disorders 1-gen-2020 Tonelli, Francesca; Bek, Jan Willem; Besio, Roberta; De Clercq, Adelbert; Leoni, Laura; Salmon, Phil; Coucke, Paul J; Willaert, Andy; Forlino, Antonella
Prolidase enzyme is required for extracellular matrix integrity and impacts on postnatal cerebellar cortex development 1-gen-2020 Insolia, V.; Priori, E. C.; Gasperini, Caterina; Coppa, F.; Cocchia, Marco; Iervasi, E.; Ferrari, B.; Besio, R.; Maruelli, S.; Bernocchi, G.; Forlino, A.; Bottone, M. G.
Knocking out TMEM38B in human foetal osteoblasts hFOB 1.19 by CRISPR/Cas9: A model for recessive OI type XIV 1-gen-2021 Leoni, L.; Tonelli, F.; Besio, R.; Gioia, R.; Moccia, F.; Rossi, A.; Forlino, A.
Targeting cellular stress in vitro improves osteoblast homeostasis, matrix collagen content and mineralization in two murine models of osteogenesis imperfecta 1-gen-2021 Garibaldi, N.; Contento, B. M.; Babini, G.; Morini, J.; Siciliani, S.; Biggiogera, M.; Raspanti, M.; Marini, J. C.; Rossi, A.; Forlino, A.; Besio, R.
Intracellular and extracellular markers of lethality in osteogenesis imperfecta: A quantitative proteomic approach 1-gen-2021 Bini, L.; Schvartz, D.; Carnemolla, C.; Besio, R.; Garibaldi, N.; Sanchez, J. -C.; Forlino, A.; Bianchi, L.
Dissecting the phenotypic variability of osteogenesis imperfecta 1-gen-2022 Garibaldi, N; Besio, R; Dalgleish, R; Villani, S; Barnes, Am; Marini, Jc; Forlino, A
The Highly Efficient Expression System of Recombinant Human Prolidase and the Effect of N-Terminal His-Tag on the Enzyme Activity 1-gen-2022 Czyrko-Horczak, Justyna; Nizioł, Magdalena; Forlino, Antonella; Besio, Roberta; Miltyk, Wojciech
Zebrafish Tric-b is required for skeletal development and bone cells differentiation 1-gen-2023 Tonelli, Francesca; Leoni, Laura; Daponte, Valentina; Gioia, Roberta; Cotti, Silvia; Fiedler, Imke A K; Larianova, Daria; Willaert, Andy; Coucke, Paul J; Villani, Simona; Busse, Björn; Besio, Roberta; Rossi, Antonio; Witten, P Eckhard; Forlino, Antonella
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