Impaired proteoglycan glycosylation, elevated TGF-β signaling, and abnormal osteoblast differentiation as the basis for bone fragility in a mouse model for gerodermia osteodysplastica

Paganini, Chiara;Rossi, Antonio;
2018-01-01

2018
Esperti anonimi
Inglese
Internazionale
ELETTRONICO
14
3
e1007242
Animals; Bone Diseases; Cell Differentiation; Decorin; Dermatan Sulfate; Disease Models, Animal; Dwarfism; Female; Fractures, Bone; Glycosylation; Mesenchymal Stem Cells; Mice, Inbred C57BL; Mice, Transgenic; Osteoblasts; Proteoglycans; Signal Transduction; Skin Diseases, Genetic; Transforming Growth Factor beta; Vesicular Transport Proteins; Ecology, Evolution, Behavior and Systematics; Molecular Biology; Genetics; Genetics (clinical); Cancer Research
http://genetics.plosjournals.org/perlserv/?request=get-archive&issn=1553-7404
23
info:eu-repo/semantics/article
262
Chan, Wing Lee; Steiner, Magdalena; Witkos, Tomasz; Egerer, Johannes; Busse, Björn; Mizumoto, Shuji; Pestka, Jan M.; Zhang, Haikuo; Hausser, Ingrid; K...espandi
1 Contributo su Rivista::1.1 Articolo in rivista
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Utilizza questo identificativo per citare o creare un link a questo documento: https://hdl.handle.net/11571/1236688
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