Hirayama's Disease (HD) is a rare condition affecting young people with a male preponderance. It is a focal distal upper arm amytrophy with unilateral or asymmetric bilateral involvement of C7, C8 and T1 spinal segments. We report a young female patient with clinical and electrophysiological findings suggestive of HD. On the basis of the clinical, EMG, and radiological findings, we have excluded a restricted form of motor neuron disease (monomelic muscular atrophy), or a limited form of multifocal motor neuropathy, and chronic left-sided cervical radiculopathy or spinal compressive disease.

Hirayama disease: Description of a clinical case in a young female patient

Cosentino G.;
2007-01-01

Abstract

Hirayama's Disease (HD) is a rare condition affecting young people with a male preponderance. It is a focal distal upper arm amytrophy with unilateral or asymmetric bilateral involvement of C7, C8 and T1 spinal segments. We report a young female patient with clinical and electrophysiological findings suggestive of HD. On the basis of the clinical, EMG, and radiological findings, we have excluded a restricted form of motor neuron disease (monomelic muscular atrophy), or a limited form of multifocal motor neuropathy, and chronic left-sided cervical radiculopathy or spinal compressive disease.
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Utilizza questo identificativo per citare o creare un link a questo documento: https://hdl.handle.net/11571/1508825
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