Sfoglia per Autore
Effect of tetracyclines on the dynamics of formation and destructuration of {beta}2-microglobulin amyloid fibrils.
2011-01-01 Giorgetti, Sofia; Raimondi, Sara; Pagano, K; Relini, A; Bucciantini, M; Corazza, A; Fogolari, F; Codutti, L; Salmona, M; Mangione, Palma; Colombo, Lino; De Luigi, A; Porcari, Riccardo; Gliozzi, A; Stefani, M; Esposito, G; Bellotti, Vittorio; Stoppini, Monica
The two tryptophans of β2-microglobulin have distinct roles in function and folding and might represent two independent responses to evolutionary pressure.
2011-01-01 Raimondi, Sara; Barbarini, Nicola; Mangione, Palma; Esposito, G; Ricagno, S; Bolognesi, M; Zorzoli, Irene; Marchese, Loredana; Soria, Cristina; Bellazzi, Riccardo; Monti, M; Stoppini, Monica; Stefanelli, Mario; Magni, Paolo; Bellotti, Vittorio
The intracellular quality control system down-regulates the secretion of amyloidogenic apolipoprotein A-I variants: A possible impact on the natural history of the disease
2011-01-01 Marchesi, Marta; Parolini, Cinzia; Valetti, Caterina; Mangione, Palma; Obici, Laura; Giorgetti, Sofia; Raimondi, Sara; Donadei, Simona; Gregorini, Gina; Merlini, Giampaolo; Stoppini, Monica; Chiesa, Giulia; Bellotti, Vittorio
Hereditary systemic amyloidosis due to Asp76Asn variant β2-microglobulin.
2012-01-01 Valleix, S; Gillmore, Jd; Bridoux, F; Mangione, Palma; Dogan, A; Nedelec, B; Boimard, M; Touchard, G; Goujon, Jm; Lacombe, C; Lozeron, P; Adams, D; Lacroix, C; Maisonobe, T; Planté Bordeneuve, V; Vrana, Ja; Theis, Jd; Giorgetti, Sofia; Porcari, Riccardo; Ricagno, S; Bolognesi, M; Stoppini, Monica; Delpech, M; Pepys, Mb; Hawkins, Pn; Bellotti, Vittorio
C. elegans expressing human beta2-microglobulin: a novel model for studying the relationship between the molecular assembly and the toxic phenotype.
2012-01-01 L., Diomede; Soria, Cristina; M., Romeo; Giorgetti, Sofia; Marchese, Loredana; Mangione, Palma; Porcari, Riccardo; Zorzoli, Irene; M., Salmona; Bellotti, Vittorio; Stoppini, Monica
Isolation and characterization of pharmaceutical grade human pentraxins, serum amyloid P component and C-reactive protein, for clinical use.
2012-01-01 Pepys, Mb; Gallimore, Jr; Lloyd, J; Li, Z; Graham, D; Taylor, Gw; Ellmerich, S; Mangione, Palma; Tennent, Ga; Hutchinson, Wl; Millar, Dj; Bennett, G; More, J; Evans, D; Mistry, Y; Poole, S; Hawkins, Pn
Benefit of doxycycline treatment on articular disability caused by dialysis related amyloidosis
2013-01-01 Montagna, G.; Cazzulani, B.; Obici, L.; Uggetti, C.; Giorgetti, Sofia; Porcari, R.; Ruggiero, R.; Mangione, Palma; Brambilla, M.; Lucchetti, J.; Guiso, G.; Gobbi, M.; Merlini, Giampaolo; Salmona, M.; Stoppini, Monica; Villa, G.; Bellotti, Vittorio
Monitoring the interaction between β2-microglobulin and the molecular chaperone αB-crystallin by NMR and mass spectrometry: αB-crystallin dissociates β2-microglobulin oligomers.
2013-01-01 Esposito, G; Garvey, M; Alverdi, V; Pettirossi, F; Corazza, A; Fogolari, F; Polano, M; Mangione, Palma; Giorgetti, Sofia; Stoppini, Monica; Rekas, A; Bellotti, Vittorio; Heck, Aj; Carver, Ja
Distribution and determinants of circulating complement factor H concentration determined by a high-throughput immunonephelometric assay
2013-01-01 Reecha, Sofat; Mangione, Palma; J., Ruth Gallimore; Svetlana, Hakobyan; Timothy R., Hughes; Tina, Shah; Tim, Goodship; Francesco, D'Aiuto; Claudia, Langenberg; Nick, Wareham; B., Paul Morgan; Mark B., Pepys; Aroon D., Hingorani
Structure, folding dynamics and amyloidogenesis of Asp76Asn β2-microglobulin: roles of shear flow, hydrophobic surfaces and α crystallin.
2013-01-01 Mangione, Palma; Esposito, G; Relini, A; Raimondi, Sara; Porcari, Riccardo; Giorgetti, Sofia; Corazza, A; Fogolari, F; Penco, A; Goto, Y; Lee, Yh; Yagi, H; Cecconi, C; Naqvi, Mm; Gillmore, Jd; Hawkins, Pn; Chiti, F; Rolandi, R; Taylor, Gw; Pepys, Mb; Stoppini, Monica; Bellotti, Vittorio
Pathogenetic mechanisms of amyloid A amyloidosis.
2013-01-01 Simons, Jp; Al Shawi, R; Ellmerich, S; Speck, I; Aslam, S; Hutchinson, Wl; Mangione, Palma; Disterer, P; Gilbertson, Ja; Hunt, T; Millar, Dj; Minogue, S; Bodin, K; Pepys, Mb; Hawkins, Pn
Class I Major Histocompatibility Complex, the Trojan horse for secretion of amyloidogenic β2-microglobulin.
2014-01-01 Halabelian, L; Ricagno, S; Giorgetti, Sofia; Santambrogio, C; Barbiroli, A; Pellegrino, S; Achour, A; Grandori, R; Marchese, Loredana; Raimondi, Sara; Mangione, Palma; Esposito, G; Al Shawi, R; Simons, Jp; Speck, I; Stoppini, Monica; Bolognesi, M; Bellotti, Vittorio
Proteolytic cleavage of Ser52Pro variant transthyretin triggers its amyloid fibrillogenesis.
2014-01-01 Mangione, Palma; Porcari, R; Gillmore, Jd; Pucci, P; Monti, M; Porcari, M; Giorgetti, Sofia; Marchese, Loredana; Raimondi, Sara; Serpell, Lc; Chen, W; Relini, A; Marcoux, J; Clatworthy, Ir; Taylor, Gw; Tennent, Ga; Robinson, Cv; Hawkins, Pn; Stoppini, Monica; Wood, Sp; Pepys, Mb; Bellotti, Vittorio
A novel mechano-enzymatic cleavage mechanism underlies transthyretin amyloidogenesis
2015-01-01 Marcoux, Julien; Mangione, Palma; Porcari, Riccardo; Degiacomi, Matteo T.; Verona, Guglielmo; Taylor, Graham W; Giorgetti, Sofia; Raimondi, Sara; Sanglier Cianférani, Sarah; Benesch, Justin Lp; Cecconi, Ciro; Naqvi, Mohsin M.; Gillmore, Julian D.; Hawkins, Philip N.; Stoppini, Monica; Robinson, Carol V.; Pepys, Mark B.; Bellotti, Vittorio
Bifunctional crosslinking ligands for transthyretin
2015-01-01 Mangione, Palma; Deroo, Stephanie; Ellmerich, Stephan; Bellotti, Vittorio; Kolstoe, Simon; Wood, Stephen P.; Robinson, Carol V.; Smith, Martin D.; Tennent, Glenys A.; Broadbridge, Robert J.; Council, Claire E.; Thurston, Joanne R.; Steadman, Victoria A.; Vong, Antonio K.; Swain, Christopher J.; Pepys, Mark B.; Taylor, Graham W.
The H50Q mutation induces a tenfold decrease in the solubility of α-synuclein.
2015-01-01 Porcari, Riccardo; Proukakis, C; Waudby, Ca; Bolognesi, B; Mangione, Palma; Paton, Jf; Mullin, S; Cabrita, Ld; Penco, A; Relini, A; Verona, Guglielmo; Vendruscolo, M; Stoppini, Monica; Tartaglia, Gg; Camilloni, C; Christodoulou, J; Schapira, Ah; Bellotti, Vittorio
Decoding the structural bases of D76N β2-microglobulin high amyloidogenicity through crystallography and asn-scan mutagenesis
2015-01-01 De Rosa, M.; Barbiroli, A.; Giorgetti, S.; Mangione, P. P.; Bolognesi, M.; Ricagno, S.
Enhanced toxicity of silver nanoparticles in transgenic Caenorhabditis elegans expressing amyloidogenic proteins
2015-01-01 Soria, Cristina; Coccini, Teresa; DE SIMONE, Uliana; Marchese, Loredana; Zorzoli, Irene; Giorgetti, Sofia; Raimondi, Sara; Mangione, Palma; Ramat, Stefano; Bellotti, Vittorio; Manzo, Luigi; Stoppini, Monica
Capillary electrophoresis analysis of different variants of the amyloidogenic protein β2 -microglobulin as a simple tool for misfolding and stability studies
2015-01-01 Bertoletti, Laura; Bisceglia, Federica; Colombo, Raffaella; Giorgetti, Sofia; Raimondi, Sara; Mangione, Palma; DE LORENZI, Ersilia
D25V apolipoprotein C-III variant causes dominant hereditary systemic amyloidosis and confers cardiovascular protective lipoprotein profile
2016-01-01 Valleix, Sophie; Verona, Guglielmo; Jourde Chiche, Noémie; Nédelec, Brigitte; Mangione, Palma; Bridoux, Frank; Mangé, Alain; Dogan, Ahmet; Goujon, Jean Michel; Lhomme, Marie; Dauteuille, Carolane; Chabert, Michèle; Porcari, Riccardo; Waudby, Christopher A; Relini, Annalisa; Talmud, Philippa J; Kovrov, Oleg; Olivecrona, Gunilla; Stoppini, Monica; Christodoulou, John; Hawkins, Philip N; Grateau, Gilles; Delpech, Marc; Kontush, Anatol; Gillmore, Julian D; Kalopissis, Athina D; Bellotti, Vittorio
Titolo | Data di pubblicazione | Autore(i) | File |
---|---|---|---|
Effect of tetracyclines on the dynamics of formation and destructuration of {beta}2-microglobulin amyloid fibrils. | 1-gen-2011 | Giorgetti, Sofia; Raimondi, Sara; Pagano, K; Relini, A; Bucciantini, M; Corazza, A; Fogolari, F; Codutti, L; Salmona, M; Mangione, Palma; Colombo, Lino; De Luigi, A; Porcari, Riccardo; Gliozzi, A; Stefani, M; Esposito, G; Bellotti, Vittorio; Stoppini, Monica | |
The two tryptophans of β2-microglobulin have distinct roles in function and folding and might represent two independent responses to evolutionary pressure. | 1-gen-2011 | Raimondi, Sara; Barbarini, Nicola; Mangione, Palma; Esposito, G; Ricagno, S; Bolognesi, M; Zorzoli, Irene; Marchese, Loredana; Soria, Cristina; Bellazzi, Riccardo; Monti, M; Stoppini, Monica; Stefanelli, Mario; Magni, Paolo; Bellotti, Vittorio | |
The intracellular quality control system down-regulates the secretion of amyloidogenic apolipoprotein A-I variants: A possible impact on the natural history of the disease | 1-gen-2011 | Marchesi, Marta; Parolini, Cinzia; Valetti, Caterina; Mangione, Palma; Obici, Laura; Giorgetti, Sofia; Raimondi, Sara; Donadei, Simona; Gregorini, Gina; Merlini, Giampaolo; Stoppini, Monica; Chiesa, Giulia; Bellotti, Vittorio | |
Hereditary systemic amyloidosis due to Asp76Asn variant β2-microglobulin. | 1-gen-2012 | Valleix, S; Gillmore, Jd; Bridoux, F; Mangione, Palma; Dogan, A; Nedelec, B; Boimard, M; Touchard, G; Goujon, Jm; Lacombe, C; Lozeron, P; Adams, D; Lacroix, C; Maisonobe, T; Planté Bordeneuve, V; Vrana, Ja; Theis, Jd; Giorgetti, Sofia; Porcari, Riccardo; Ricagno, S; Bolognesi, M; Stoppini, Monica; Delpech, M; Pepys, Mb; Hawkins, Pn; Bellotti, Vittorio | |
C. elegans expressing human beta2-microglobulin: a novel model for studying the relationship between the molecular assembly and the toxic phenotype. | 1-gen-2012 | L., Diomede; Soria, Cristina; M., Romeo; Giorgetti, Sofia; Marchese, Loredana; Mangione, Palma; Porcari, Riccardo; Zorzoli, Irene; M., Salmona; Bellotti, Vittorio; Stoppini, Monica | |
Isolation and characterization of pharmaceutical grade human pentraxins, serum amyloid P component and C-reactive protein, for clinical use. | 1-gen-2012 | Pepys, Mb; Gallimore, Jr; Lloyd, J; Li, Z; Graham, D; Taylor, Gw; Ellmerich, S; Mangione, Palma; Tennent, Ga; Hutchinson, Wl; Millar, Dj; Bennett, G; More, J; Evans, D; Mistry, Y; Poole, S; Hawkins, Pn | |
Benefit of doxycycline treatment on articular disability caused by dialysis related amyloidosis | 1-gen-2013 | Montagna, G.; Cazzulani, B.; Obici, L.; Uggetti, C.; Giorgetti, Sofia; Porcari, R.; Ruggiero, R.; Mangione, Palma; Brambilla, M.; Lucchetti, J.; Guiso, G.; Gobbi, M.; Merlini, Giampaolo; Salmona, M.; Stoppini, Monica; Villa, G.; Bellotti, Vittorio | |
Monitoring the interaction between β2-microglobulin and the molecular chaperone αB-crystallin by NMR and mass spectrometry: αB-crystallin dissociates β2-microglobulin oligomers. | 1-gen-2013 | Esposito, G; Garvey, M; Alverdi, V; Pettirossi, F; Corazza, A; Fogolari, F; Polano, M; Mangione, Palma; Giorgetti, Sofia; Stoppini, Monica; Rekas, A; Bellotti, Vittorio; Heck, Aj; Carver, Ja | |
Distribution and determinants of circulating complement factor H concentration determined by a high-throughput immunonephelometric assay | 1-gen-2013 | Reecha, Sofat; Mangione, Palma; J., Ruth Gallimore; Svetlana, Hakobyan; Timothy R., Hughes; Tina, Shah; Tim, Goodship; Francesco, D'Aiuto; Claudia, Langenberg; Nick, Wareham; B., Paul Morgan; Mark B., Pepys; Aroon D., Hingorani | |
Structure, folding dynamics and amyloidogenesis of Asp76Asn β2-microglobulin: roles of shear flow, hydrophobic surfaces and α crystallin. | 1-gen-2013 | Mangione, Palma; Esposito, G; Relini, A; Raimondi, Sara; Porcari, Riccardo; Giorgetti, Sofia; Corazza, A; Fogolari, F; Penco, A; Goto, Y; Lee, Yh; Yagi, H; Cecconi, C; Naqvi, Mm; Gillmore, Jd; Hawkins, Pn; Chiti, F; Rolandi, R; Taylor, Gw; Pepys, Mb; Stoppini, Monica; Bellotti, Vittorio | |
Pathogenetic mechanisms of amyloid A amyloidosis. | 1-gen-2013 | Simons, Jp; Al Shawi, R; Ellmerich, S; Speck, I; Aslam, S; Hutchinson, Wl; Mangione, Palma; Disterer, P; Gilbertson, Ja; Hunt, T; Millar, Dj; Minogue, S; Bodin, K; Pepys, Mb; Hawkins, Pn | |
Class I Major Histocompatibility Complex, the Trojan horse for secretion of amyloidogenic β2-microglobulin. | 1-gen-2014 | Halabelian, L; Ricagno, S; Giorgetti, Sofia; Santambrogio, C; Barbiroli, A; Pellegrino, S; Achour, A; Grandori, R; Marchese, Loredana; Raimondi, Sara; Mangione, Palma; Esposito, G; Al Shawi, R; Simons, Jp; Speck, I; Stoppini, Monica; Bolognesi, M; Bellotti, Vittorio | |
Proteolytic cleavage of Ser52Pro variant transthyretin triggers its amyloid fibrillogenesis. | 1-gen-2014 | Mangione, Palma; Porcari, R; Gillmore, Jd; Pucci, P; Monti, M; Porcari, M; Giorgetti, Sofia; Marchese, Loredana; Raimondi, Sara; Serpell, Lc; Chen, W; Relini, A; Marcoux, J; Clatworthy, Ir; Taylor, Gw; Tennent, Ga; Robinson, Cv; Hawkins, Pn; Stoppini, Monica; Wood, Sp; Pepys, Mb; Bellotti, Vittorio | |
A novel mechano-enzymatic cleavage mechanism underlies transthyretin amyloidogenesis | 1-gen-2015 | Marcoux, Julien; Mangione, Palma; Porcari, Riccardo; Degiacomi, Matteo T.; Verona, Guglielmo; Taylor, Graham W; Giorgetti, Sofia; Raimondi, Sara; Sanglier Cianférani, Sarah; Benesch, Justin Lp; Cecconi, Ciro; Naqvi, Mohsin M.; Gillmore, Julian D.; Hawkins, Philip N.; Stoppini, Monica; Robinson, Carol V.; Pepys, Mark B.; Bellotti, Vittorio | |
Bifunctional crosslinking ligands for transthyretin | 1-gen-2015 | Mangione, Palma; Deroo, Stephanie; Ellmerich, Stephan; Bellotti, Vittorio; Kolstoe, Simon; Wood, Stephen P.; Robinson, Carol V.; Smith, Martin D.; Tennent, Glenys A.; Broadbridge, Robert J.; Council, Claire E.; Thurston, Joanne R.; Steadman, Victoria A.; Vong, Antonio K.; Swain, Christopher J.; Pepys, Mark B.; Taylor, Graham W. | |
The H50Q mutation induces a tenfold decrease in the solubility of α-synuclein. | 1-gen-2015 | Porcari, Riccardo; Proukakis, C; Waudby, Ca; Bolognesi, B; Mangione, Palma; Paton, Jf; Mullin, S; Cabrita, Ld; Penco, A; Relini, A; Verona, Guglielmo; Vendruscolo, M; Stoppini, Monica; Tartaglia, Gg; Camilloni, C; Christodoulou, J; Schapira, Ah; Bellotti, Vittorio | |
Decoding the structural bases of D76N β2-microglobulin high amyloidogenicity through crystallography and asn-scan mutagenesis | 1-gen-2015 | De Rosa, M.; Barbiroli, A.; Giorgetti, S.; Mangione, P. P.; Bolognesi, M.; Ricagno, S. | |
Enhanced toxicity of silver nanoparticles in transgenic Caenorhabditis elegans expressing amyloidogenic proteins | 1-gen-2015 | Soria, Cristina; Coccini, Teresa; DE SIMONE, Uliana; Marchese, Loredana; Zorzoli, Irene; Giorgetti, Sofia; Raimondi, Sara; Mangione, Palma; Ramat, Stefano; Bellotti, Vittorio; Manzo, Luigi; Stoppini, Monica | |
Capillary electrophoresis analysis of different variants of the amyloidogenic protein β2 -microglobulin as a simple tool for misfolding and stability studies | 1-gen-2015 | Bertoletti, Laura; Bisceglia, Federica; Colombo, Raffaella; Giorgetti, Sofia; Raimondi, Sara; Mangione, Palma; DE LORENZI, Ersilia | |
D25V apolipoprotein C-III variant causes dominant hereditary systemic amyloidosis and confers cardiovascular protective lipoprotein profile | 1-gen-2016 | Valleix, Sophie; Verona, Guglielmo; Jourde Chiche, Noémie; Nédelec, Brigitte; Mangione, Palma; Bridoux, Frank; Mangé, Alain; Dogan, Ahmet; Goujon, Jean Michel; Lhomme, Marie; Dauteuille, Carolane; Chabert, Michèle; Porcari, Riccardo; Waudby, Christopher A; Relini, Annalisa; Talmud, Philippa J; Kovrov, Oleg; Olivecrona, Gunilla; Stoppini, Monica; Christodoulou, John; Hawkins, Philip N; Grateau, Gilles; Delpech, Marc; Kontush, Anatol; Gillmore, Julian D; Kalopissis, Athina D; Bellotti, Vittorio |
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